Pediatric-Perinatal Pathology Index

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    Malformations and Deformations:

    External Anomalies
  1. Cleft lip, gross
  2. Lateral cleft lip, gross
  3. Facial abnormalities, gross
  4. Hands with abnormal crease, gross
  5. Syndactyly, hand and foot, gross
  6. Syndactyly, hand, gross
  7. Clenched hand, gross
  8. 'Rocker bottom' foot, gross
  9. Sirenomelia, gross
  10. Intrauterine fetal demise, external features, gross
  11. Hydrops fetalis, gross [XRAY]
  12. Abdominal Anomalies
  13. Omphalocele, gross
  14. Gastroschisis, gross
  15. Limb-body wall complex, gross [XRAY]
  16. Limb-body wall complex, gross
  17. Bowel atresia, gross
  18. Duodenal atresia, gross [XRAY]
  19. Colonic atresia, gross
  20. Tracheo-esophageal fistula and atresia, gross
  21. Diaphragmatic hernia, gross
  22. Diaphragmatic hernia, gross
  23. Renal Anomalies and Oligohydramnios Sequence
  24. Recessive polycystic kidney disease, gross
  25. Renal agenesis, gross
  26. 'Potter facies' from oligohydramnios, gross
  27. 'Potter facies' and 'glove-like' hand from oligohydramnios, gross
  28. Normal chest cavity, gross
  29. Pulmonary hypoplasia, gross
  30. Pulmonary hypoplasia, microscopic
  31. Varus deformities, feet, gross
  32. Central Nervous System Anomalies
  33. Alobar holoprosencephaly, gross [MRI]
  34. Semilobar holoprosencephaly, gross
  35. Holoprosencephaly, gross
  36. Hydranencephaly, gross


  37. Abnormalities of Twinning:

  38. Siamese twins (craniothoracopagus), gross
  39. Siamese twins (thoracopagus ), gross
  40. Acardius acephalus (chorangiopagus parasiticus), gross
  41. Acardius anceps (chorangiopagus parasiticus), gross
  42. Twin-twin transfusion syndrome, gross


  43. Neural Tube Defects:

  44. Meningomyelocele, gross
  45. Meningomyelocele, gross
  46. Anencephaly, gross
  47. Anencephaly, gross
  48. Anencephaly, gross
  49. Iniencephaly, gross
  50. Rachischisis, gross
  51. Iniencephaly, encephalocele, rachischisis, gross
  52. Exencephaly, gross


  53. Pediatric Neoplasia:

  54. Nasopharyngeal teratoma, congenital, gross
  55. Teratoma, congenital, low power microscopic
  56. Lymphangioma, congenital, gross
  57. Lymphangioma, congenital, medium power microscopic
  58. Lymphangioma, congenital, medium power microscopic
  59. Hemangioma, congenital, gross
  60. Wilms tumor, gross
  61. Wilms tumor, medium power microscopic
  62. Neuroblastoma, gross [MRI]
  63. Neuroblastoma, medium power microscopic
  64. Rhabdomyosarcoma, low power microscopic [CT]
  65. Rhabdomyosarcoma, medium power microscopic [MRI]


  66. Congenital Infections:

  67. Congenital syphilis, gumma in heart, gross
  68. Spirochetes (Treponema pallidum), microscopic
  69. Cytomegalovirus, congenital, kidney, microscopic
  70. Parvovirus, congenital, spleen, microscopic
  71. Congenital pneumonia, microscopic


  72. Complications of Prematurity:

  73. Hyaline membrane disease, lung, microscopic [XRAY]
  74. Bronchopulmonary dysplasia, lung, microscopic [MRI]
  75. Germinal matrix, brain, normal and with hemorrhage, low power microscopic
  76. Intraventricular hemorrhage, gross
  77. Intraventricular hemorrhage, severe, gross
  78. Kernicterus, brain, gross
  79. Neonatal necrotizing enterocolitis (NEC), gross
  80. Neonatal necrotizing enterocolitis (NEC) and normal bowel, low power microscopic


  81. Miscellaneous Conditions:

  82. Pyloric stenosis, gross
  83. Meconium ileus, gross
  84. Meconium ileus with peritonitis, gross
  85. Hirschsprung disease, gross
  86. Pneumatosis intestinalis, microscopic
  87. Normal skin with hair, gross
  88. Accessory spleens, gross
  89. Postmaturity with prominent fingernails, gross
  90. Maceration, gross
  91. Fetal chest with thymus, gross
  92. Thymus with macrophages, low power microscopic
  93. Subgaleal hemorrhage, gross
  94. Meconium aspiration, medium power microscopic
  95. Meconium aspiration, high power microscopic

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