Dermatology Anatomy / Physiology Clinical Abnormalities--Epidermis

Recessive epidermolysis bullosa

John L. Bezzant, M.D.

Same child with recessive epidermolysis bullosa. The slightest abrasion on the skin would tear the epidermis from the underlying dermis, and this was true of the mucosa as well. The child had broad areas of dermis that were exposed, and the child was treated as a burn victim with Silvadene cream and Vaseline wraps on top of that. The exposed dermis makes it difficult to control body temperature, body fluids, and secondary infection is a constant problem.